Respiratory involvement in juvenile dermatomyositis
نویسندگان
چکیده
منابع مشابه
Respiratory involvement in juvenile dermatomyositis
Materials and methods 16 patients (9 girls) with diagnosis of JDM (age 3–16,2 yrs) performed pulmonary function tests (PFT). 14 were receiving treatment; all had muscular testing. 13 had weakness as major symptom. Respiratory symptoms: dry cough in 2/16; reduced exercise tolerance: 3/16. Chest xray: normal in 13/13. Echocardiogram and ECG: normal in all. 9/16 had positive ANA-Ab; antiJO1 Ab neg...
متن کاملDramatic heliotrope dermatitis and uncommon pulmonary involvement in juvenile dermatomyositis.
and interstitial lung disease is frequently identifi ed abnormality by CT. 3 Here we present a JDM case with severe heliotrope rash and uncommon manifestation in CT image of the lung. A 15-year-old girl presented with a 3-month history of progressive periorbital swelling and a reddishpurple rash on the upper and lower eyelids ( fi gure 1A ). Her vision acuity decreased and MRI showed only thick...
متن کاملJuvenile dermatomyositis.
Juvenile dermatomyositis (JDMS) is a chronic inflammatory condition characterized by muscle weakness and a distinctive rash caused by underlying vasculopathy. Long-term complications include subcutaneous and muscular calcification, contractures and in some cases the gradual development of a second connective tissue disease. Early aggressive treatment with systemic immunosuppressants and other a...
متن کاملJuvenile dermatomyositis.
The clinical profile of 7 children and their follow-up is described. There was female preponderance with mate to female ratio of 1:6. The median age of onset was 6 years. All the patients had skin rash, muscle weakness and abnormal enzyme profile. Muscle biopsy was performed in 6 and was abnormal in all of them. The electromyogram (EMG) was performed in 6 and was found abnormal in five. All the...
متن کاملJuvenile Dermatomyositis in Pregnancy
Juvenile dermatomyositis has variable clinical presentations both in and outside of pregnancy. A literature review indicated that optimal maternal and fetal outcomes can be anticipated when the pregnancy is undertaken while the disease is in remission. Poorer outcomes are associated with flare-up of the disease in early pregnancy compared with exacerbation in the second or third trimester, when...
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ژورنال
عنوان ژورنال: Pediatric Rheumatology
سال: 2008
ISSN: 1546-0096
DOI: 10.1186/1546-0096-6-s1-p219